ABSTRACT
Two-dimensional Doppler echocardiographic velocity profiles of four cardiac valves in a group of 85 infants and children with left to right shunt lesions(VSD, ASD and PDA) are presented. Velocities were obtained before operation and 10 days afterward. The results were as follows ; 1) VSD(type 2) Peak velocities of mitral valve were significantly decreased when compared preop. with postop. echocardiogram(n=37, preop 132+/-24, postop 98+/-16 cm/sec, p0.05). Aortic valve velocities showed no significant changes (n=10, perop 134+/-23, postop 121+/-25cm/sec, p>0.05). Peak velocities of pulmonic valve were significantly decreased(n=28, perop 138+/-37, postop 107+/-27cm/sec, p<0.005). This study demonstrates that Doppler echocardiographic assessment of velovity changes are correlated with known hemodynamic data and also will be a good index in the evaluation of operation.
Subject(s)
Child , Humans , Infant , Aortic Valve , Echocardiography , Echocardiography, Doppler , Heart Valves , Hemodynamics , Mitral Valve , Tricuspid ValveABSTRACT
Williams syndrome is a progressive and multisystemic disorder. We experienced one case of Willams syndrome which was characterized by elfin facies, mental retardation, diffuse aortic hypoplasia, mitral regurgitation and chronic nonparoxysmal sinus tachycardia. The tachycardia has been managing with beta-blocker successfully. We presented a case of unusual form of Williams syndrome with a reivew of literatures.
Subject(s)
Facies , Intellectual Disability , Mitral Valve Insufficiency , Tachycardia , Tachycardia, Sinus , Williams SyndromeABSTRACT
No abstract available.
Subject(s)
Empyema, Subdural , Haemophilus influenzae , Haemophilus , MeningitisABSTRACT
No abstract available.
Subject(s)
Child , Humans , Aorta, Thoracic , Echocardiography, DopplerABSTRACT
Thirty - five cases of coarctation of aorta, diagnosed by cardiac catheterization and angiography during the period of 1980-1984, at the department of Pediatrics of Seoul National University Hospital, were studied on the clinical features and management. The followoing results were obtained : 1) The incidence of coartation of aorta was 1.2% of congenital heart disease and sex ratio of male to female was 2.2 : 1. 2) The anatomical type of coarctation was preductal in 19 cases, juxtaductal in 15 cases and postductal in 1 case. Most of preductal coarctation (89.5%) were associated with aortic arch or isthmus hypoplasia. 3) All of these patients had various type of additional cardiac anomalies and among them, PDA was the most common associated lesion and followed by VSD. 4) Significant BP gradient between upper and lower extremies and weak femoral pulsation were noticed in 15 cases(42.8%). 5) Congestive heart failure was present in all but one patient less than 1 year old, while only 3 cases(15%) had congestive heat failure in patients older than one year. 6) Overall surgical mortality was 31.8%, but significant decrease in surgical mortality was found since 1983.
Subject(s)
Female , Humans , Male , Angiography , Aorta , Aorta, Thoracic , Aortic Coarctation , Cardiac Catheterization , Cardiac Catheters , Estrogens, Conjugated (USP) , Heart Defects, Congenital , Heart Failure , Hot Temperature , Incidence , Mortality , Pediatrics , Seoul , Sex RatioABSTRACT
Premature separation of the placenta(abruptio placentae), as a serious obstetric complication, has been recognized to be associated with disseminated intravascular coagulation(DIC) in the newborn period. However, pathologic evidence for DIC generally has been lacking or rarely reported. Recently we have experienced one case of DIC in an infant born after abruptio placentae. The infant had suffered from cyanosis, dyspnea and convulsion. The peripheral blood smear of this infant revealed severe thrombocytopenia, but there was no evidence of external bleeding. At autopsy widespread hyaline thrombi were observed in the small vessels and capillaries of the brain and liver. The brain showed diffuse cortical and subcortical white matter necrosis associated with hemorrhage. Bilateral symmetrical necrosis of the thalamus was also seen. Massive fresh hemorrhage was present in the endometrium and myometrium. We considered tha tthe above findings were consistent with DIC. Pertinent literatures on neonatal DIC are also reviewed briefly.
Subject(s)
Animals , Female , Humans , Infant , Infant, Newborn , Mice , Pregnancy , Abruptio Placentae , Autopsy , Brain , Capillaries , Cyanosis , Dacarbazine , Disseminated Intravascular Coagulation , Dyspnea , Endometrium , Hemorrhage , Hyalin , Liver , Myometrium , Necrosis , Seizures , Thalamus , ThrombocytopeniaABSTRACT
No abstract available.
ABSTRACT
Histiocytic Medullary Reticulosis(H.M.R.) is a rapidly progressing fatal disease seen most often in adults, but it has been reported in children younger than 15 years of age. H.M.R. is clinically characterized by fever, wasting generalized lymphadenopathy and hepatosplenomegaly. In the terminal stage, jaundice, purpura, anemia and pancytopenia are all present with or without skin involvement. Cardinal pathologic features are systemized proliferation of atypical, neoplastic, erythrophagocytic histiocytes and their precursors throughout the lymphoreticular tissues. Four cases of H.M.R. occurring in pediatric age group, i.e., 5 years, 6 years, 12 years and 14 years of age, respectively, are presented with discussion of the clinico-pathologic characteristics and management. Cases 1,2 and 3 died within 6 months after the onset of illness. Case 1 of our series was particularly younger than in previously reported cases. This was the case that the diagnosis was confirmed by postmortem examination. Analysis of previously reported 25 cases occurring in ages younger than 20 years of age was done.